Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004561363 | SCV005048993 | uncertain significance | Dyskeratosis congenita | 2024-02-22 | criteria provided, single submitter | clinical testing | The p.S290F variant (also known as c.869C>T), located in coding exon 2 of the TERT gene, results from a C to T substitution at nucleotide position 869. The serine at codon 290 is replaced by phenylalanine, an amino acid with highly dissimilar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this alteration remains unclear. |