Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001919364 | SCV002189943 | pathogenic | Acrocallosal syndrome | 2022-06-05 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 1422094). This premature translational stop signal has been observed in individual(s) with acrocallosal syndrome (PMID: 26349186). This variant is present in population databases (rs772716663, gnomAD 0.003%). This sequence change creates a premature translational stop signal (p.Leu568Profs*21) in the KIF7 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in KIF7 are known to be pathogenic (PMID: 19666503, 21552264, 21633164, 26648833). |