Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV004723691 | SCV005329359 | uncertain significance | Congenital myasthenic syndrome 8 | 2023-05-20 | criteria provided, single submitter | clinical testing | The observed missense c.1555G>T(p.Ala519Ser) variant in AGRN gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is reported with the allele frequency of 0.0004% in the gnomAD Exomes. The amino acid Ala at position 519 is changed to a Ser changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Ala519Ser in AGRN is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. Computational evidence (SIFT - Tolerated, and MutationTaster - Disease causing) predicts conflicting evidence on protein structure and function for this variant. For these reasons, this variant has been classified as Uncertain Significance. |