Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004645008 | SCV005132881 | uncertain significance | Inborn genetic diseases | 2024-04-22 | criteria provided, single submitter | clinical testing | The p.H1254P variant (also known as c.3761A>C), located in coding exon 27 of the LRRK2 gene, results from an A to C substitution at nucleotide position 3761. The histidine at codon 1254 is replaced by proline, an amino acid with similar properties. This amino acid position is conserved. In addition, this alteration is predicted to be tolerated by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |