Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000194408 | SCV000247494 | pathogenic | Bilateral frontoparietal polymicrogyria | 2013-02-08 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001220464 | SCV001392453 | pathogenic | not provided | 2019-06-07 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Leu406Serfs*42) in the ADGRG1 gene. It is expected to result in an absent or disrupted protein product. For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in ADGRG1 are known to be pathogenic (PMID: 15044805, 20929962). This variant has been observed in an individual affected with bilateral frontoparietal polymicrogyria (PMID: 20929962). ClinVar contains an entry for this variant (Variation ID: 211093). This variant is not present in population databases (ExAC no frequency). |