Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV003338911 | SCV004047295 | likely pathogenic | Combined immunodeficiency due to DOCK8 deficiency | criteria provided, single submitter | clinical testing | The frame shift variant c.5455_5458dup (p.Thr1820AsnfsTer6) in DOCK8 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. The p.Thr1820AsnfsTer6 variant is novel (not in any individuals) in gnomAD Exomes and 1000 Genomes. This variant causes a frameshift starting with codon Threonine 1820, changes this amino acid to Asparagine residue, and creates a premature Stop codon at position 6 of the new reading frame, denoted p.Thr1820AsnfsTer6. Loss of function variants have been previously reported to be disease causing. For these reasons, this variant has been classified as Likely Pathogenic. |