Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000986514 | SCV001135529 | uncertain significance | Usher syndrome type 2A | 2019-05-28 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001041834 | SCV001205479 | likely pathogenic | not provided | 2024-01-28 | criteria provided, single submitter | clinical testing | This sequence change replaces proline, which is neutral and non-polar, with leucine, which is neutral and non-polar, at codon 5127 of the USH2A protein (p.Pro5127Leu). This variant is present in population databases (rs201513512, gnomAD 0.003%). This missense change has been observed in individuals with clinical features of retinitis pigmentosa (Invitae). ClinVar contains an entry for this variant (Variation ID: 801608). Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) has been performed at Invitae for this missense variant, however the output from this modeling did not meet the statistical confidence thresholds required to predict the impact of this variant on USH2A protein function. In summary, the currently available evidence indicates that the variant is pathogenic, but additional data are needed to prove that conclusively. Therefore, this variant has been classified as Likely Pathogenic. |
Blueprint Genetics | RCV001074615 | SCV001240206 | uncertain significance | Retinal dystrophy | 2019-01-28 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV001328877 | SCV001520109 | uncertain significance | Retinitis pigmentosa 39 | 2019-04-09 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Ce |
RCV001041834 | SCV001746893 | uncertain significance | not provided | 2021-04-01 | criteria provided, single submitter | clinical testing | |
Natera, |
RCV000986514 | SCV002088187 | uncertain significance | Usher syndrome type 2A | 2020-08-04 | no assertion criteria provided | clinical testing |