Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000041905 | SCV000065601 | pathogenic | Rare genetic deafness | 2012-06-14 | criteria provided, single submitter | clinical testing | The Ser2415X variant in USH2A has not been reported in the literature nor previo usly identified by our laboratory. This nonsense variant leads to a premature te rmination codon at position 2415 which is predicted to lead to a truncated or ab sent protein. In summary, this variant meets our criteria to be classified as pa thogenic (http://pcpgm.partners.org/LMM). |
Labcorp Genetics |
RCV001205092 | SCV001376328 | pathogenic | not provided | 2024-10-17 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Ser2415*) in the USH2A gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in USH2A are known to be pathogenic (PMID: 10729113, 10909849, 20507924, 25649381). This variant is not present in population databases (gnomAD no frequency). This variant has not been reported in the literature in individuals affected with USH2A-related conditions. ClinVar contains an entry for this variant (Variation ID: 48579). For these reasons, this variant has been classified as Pathogenic. |
Genome- |
RCV003450885 | SCV004183276 | pathogenic | Usher syndrome type 2A | 2023-11-04 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV003466893 | SCV004206354 | pathogenic | Retinitis pigmentosa 39 | 2023-01-12 | criteria provided, single submitter | clinical testing |