Total submissions: 8
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000669141 | SCV000793857 | pathogenic | Usher syndrome type 2A; Retinitis pigmentosa 39 | 2017-09-11 | criteria provided, single submitter | clinical testing | |
Blueprint Genetics | RCV001073245 | SCV001238781 | pathogenic | Retinal dystrophy | 2018-08-29 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001389152 | SCV001590418 | pathogenic | not provided | 2022-04-14 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 553648). This premature translational stop signal has been observed in individual(s) with Usher syndrome and inherited retinal disease (PMID: 26927203, 27160483). This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Trp2693*) in the USH2A gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in USH2A are known to be pathogenic (PMID: 10729113, 10909849, 20507924, 25649381). |
Genome- |
RCV003453281 | SCV004182849 | pathogenic | Retinitis pigmentosa 39 | 2023-11-04 | criteria provided, single submitter | clinical testing | |
Genome- |
RCV003453280 | SCV004182850 | pathogenic | Usher syndrome type 2A | 2023-11-04 | criteria provided, single submitter | clinical testing | |
Clinical Genetics, |
RCV001389152 | SCV001920103 | pathogenic | not provided | no assertion criteria provided | clinical testing | ||
Joint Genome Diagnostic Labs from Nijmegen and Maastricht, |
RCV001389152 | SCV001957410 | pathogenic | not provided | no assertion criteria provided | clinical testing | ||
Clinical Genetics DNA and cytogenetics Diagnostics Lab, |
RCV001389152 | SCV001964742 | pathogenic | not provided | no assertion criteria provided | clinical testing |