Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV003718285 | SCV004509493 | pathogenic | not provided | 2023-12-21 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Trp1770*) in the FREM2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in FREM2 are known to be pathogenic (PMID: 18203166, 26552811). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with cryptophthalmos (PMID: 30802441). ClinVar contains an entry for this variant (Variation ID: 625183). For these reasons, this variant has been classified as Pathogenic. |
OMIM | RCV000767224 | SCV000897768 | pathogenic | Isolated cryptophthalmia | 2019-04-10 | no assertion criteria provided | literature only |