Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genetic Services Laboratory, |
RCV000043572 | SCV000597293 | likely pathogenic | Microcephaly-capillary malformation syndrome | 2017-04-19 | criteria provided, single submitter | clinical testing | |
Gene |
RCV004719680 | SCV005325161 | likely pathogenic | not provided | 2023-06-15 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 21815250, 23542699) |
OMIM | RCV000043572 | SCV000071442 | pathogenic | Microcephaly-capillary malformation syndrome | 2013-05-01 | no assertion criteria provided | literature only |