If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
affects |
association |
not provided |
total |
131
|
108
|
1183
|
381
|
249
|
7
|
1
|
1
|
2050
|
Gene and significance breakdown #
Total genes and gene combinations: 101
Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
affects |
association |
not provided |
total |
SACS
|
10
|
7
|
88
|
36
|
13
|
0 |
0 |
0 |
153
|
SPG11
|
28
|
21
|
71
|
17
|
15
|
0 |
0 |
0 |
149
|
ZFYVE26
|
6
|
4
|
59
|
29
|
21
|
0 |
0 |
0 |
119
|
USP8
|
0 |
0 |
53
|
37
|
19
|
0 |
0 |
0 |
109
|
AP5Z1
|
2
|
4
|
72
|
12
|
13
|
0 |
0 |
0 |
103
|
KIF1A
|
4
|
3
|
55
|
18
|
11
|
0 |
0 |
0 |
91
|
SPAST
|
26
|
20
|
24
|
2
|
2
|
0 |
0 |
0 |
74
|
TECPR2
|
1
|
2
|
51
|
12
|
8
|
0 |
0 |
0 |
74
|
SETX
|
0 |
0 |
47
|
18
|
6
|
0 |
0 |
0 |
71
|
SPG7
|
15
|
6
|
30
|
8
|
7
|
0 |
0 |
0 |
66
|
KIF1C
|
0 |
1
|
39
|
6
|
9
|
0 |
0 |
0 |
53
|
PNPLA6
|
1
|
2
|
30
|
10
|
7
|
0 |
0 |
0 |
50
|
KIF5A
|
3
|
4
|
19
|
11
|
6
|
0 |
0 |
1
|
42
|
ALS2
|
0 |
0 |
32
|
6
|
3
|
0 |
0 |
0 |
41
|
WASHC5
|
0 |
1
|
27
|
6
|
4
|
0 |
0 |
0 |
38
|
POLG, POLGARF
|
0 |
1
|
22
|
6
|
3
|
0 |
0 |
0 |
32
|
AP4E1
|
0 |
0 |
22
|
7
|
1
|
0 |
0 |
0 |
30
|
PGAP1
|
0 |
0 |
21
|
5
|
4
|
0 |
0 |
0 |
30
|
ALDH18A1
|
0 |
1
|
17
|
5
|
5
|
0 |
0 |
0 |
28
|
DDHD1
|
1
|
0 |
20
|
4
|
3
|
0 |
0 |
0 |
28
|
CYP2U1
|
1
|
2
|
19
|
3
|
2
|
0 |
0 |
0 |
27
|
GBA2
|
2
|
1
|
17
|
3
|
4
|
0 |
0 |
0 |
27
|
L1CAM
|
0 |
0 |
11
|
12
|
4
|
0 |
0 |
0 |
27
|
AP4M1
|
1
|
0 |
20
|
1
|
4
|
0 |
0 |
0 |
26
|
CYP7B1
|
5
|
4
|
13
|
3
|
2
|
0 |
0 |
0 |
26
|
DDHD2
|
1
|
2
|
14
|
8
|
1
|
0 |
0 |
0 |
26
|
POLG
|
5
|
2
|
8
|
5
|
6
|
0 |
0 |
0 |
26
|
USP50, USP8
|
0 |
0 |
14
|
7
|
4
|
0 |
0 |
0 |
25
|
AP4B1
|
0 |
1
|
14
|
4
|
5
|
0 |
0 |
0 |
24
|
BSCL2, HNRNPUL2-BSCL2
|
1
|
0 |
20
|
2
|
1
|
0 |
0 |
0 |
24
|
FA2H
|
1
|
2
|
11
|
3
|
7
|
0 |
0 |
0 |
24
|
ENTPD1
|
0 |
0 |
18
|
2
|
1
|
0 |
0 |
0 |
21
|
HSPD1
|
0 |
0 |
8
|
6
|
7
|
0 |
0 |
0 |
21
|
TWNK
|
0 |
0 |
16
|
3
|
1
|
0 |
0 |
0 |
20
|
ATL1
|
3
|
4
|
2
|
7
|
3
|
0 |
0 |
0 |
19
|
GJC2
|
0 |
0 |
11
|
6
|
2
|
0 |
0 |
0 |
19
|
REEP1
|
5
|
5
|
6
|
2
|
1
|
0 |
0 |
0 |
19
|
SPG21
|
1
|
2
|
15
|
0 |
1
|
0 |
0 |
0 |
19
|
SPART
|
0 |
0 |
15
|
2
|
1
|
0 |
0 |
0 |
18
|
RTN2
|
0 |
0 |
7
|
6
|
4
|
0 |
0 |
0 |
17
|
VPS37A
|
0 |
0 |
10
|
4
|
2
|
0 |
0 |
0 |
16
|
MILR1, POLG2
|
0 |
0 |
8
|
4
|
2
|
0 |
0 |
0 |
14
|
C19orf12
|
2
|
0 |
6
|
1
|
2
|
0 |
0 |
0 |
11
|
ERLIN2
|
3
|
1
|
6
|
0 |
2
|
0 |
0 |
0 |
11
|
MTRFR
|
0 |
0 |
7
|
3
|
1
|
0 |
0 |
0 |
11
|
SLC33A1
|
0 |
0 |
5
|
5
|
1
|
0 |
0 |
0 |
11
|
ERLIN1
|
0 |
1
|
7
|
2
|
0 |
0 |
0 |
0 |
10
|
SLC16A2
|
0 |
1
|
4
|
4
|
1
|
0 |
0 |
0 |
10
|
NIPA1
|
1
|
0 |
5
|
1
|
1
|
0 |
0 |
0 |
8
|
KIF1C, LOC126862473
|
0 |
0 |
4
|
1
|
2
|
0 |
0 |
0 |
7
|
LOC130056709, NIPA1
|
0 |
0 |
3
|
4
|
1
|
0 |
0 |
0 |
7
|
AP4S1
|
0 |
0 |
3
|
3
|
0 |
0 |
0 |
0 |
6
|
LOC130059818, SPG7
|
0 |
0 |
4
|
0 |
2
|
0 |
0 |
0 |
6
|
CNNM2, NT5C2
|
0 |
0 |
3
|
1
|
1
|
0 |
0 |
0 |
5
|
LOC126860498, WASHC5
|
0 |
0 |
2
|
2
|
1
|
0 |
0 |
0 |
5
|
PLP1, RAB9B
|
1
|
0 |
3
|
0 |
1
|
0 |
0 |
0 |
5
|
FANCI, POLG
|
0 |
0 |
1
|
0 |
3
|
0 |
0 |
0 |
4
|
KIF1A, LOC126806583
|
0 |
0 |
2
|
2
|
0 |
0 |
0 |
0 |
4
|
NT5C2
|
0 |
0 |
4
|
0 |
0 |
0 |
0 |
0 |
4
|
AP5B1
|
0 |
0 |
3
|
0 |
0 |
0 |
0 |
0 |
3
|
KIF1C, LOC126862472
|
0 |
0 |
2
|
1
|
0 |
0 |
0 |
0 |
3
|
LOC130009366, SACS
|
0 |
0 |
3
|
0 |
0 |
0 |
0 |
0 |
3
|
MAG
|
0 |
0 |
3
|
0 |
0 |
0 |
0 |
0 |
3
|
MCOLN1, PNPLA6
|
0 |
0 |
0 |
0 |
3
|
0 |
0 |
0 |
3
|
AP4B1, DCLRE1B, LOC129931235
|
0 |
0 |
2
|
0 |
0 |
0 |
0 |
0 |
2
|
AP5Z1, LOC129997861
|
0 |
0 |
0 |
1
|
1
|
0 |
0 |
0 |
2
|
ARSI
|
0 |
0 |
2
|
0 |
0 |
0 |
0 |
0 |
2
|
BICD2
|
0 |
0 |
2
|
0 |
0 |
0 |
0 |
0 |
2
|
CYP2U1, LOC129992929
|
0 |
0 |
1
|
0 |
1
|
0 |
0 |
0 |
2
|
FA2H, LOC130059394
|
0 |
0 |
2
|
0 |
0 |
0 |
0 |
0 |
2
|
LOC130064702, RTN2
|
0 |
0 |
2
|
0 |
0 |
0 |
0 |
0 |
2
|
ADAM28, ADAM7
|
0 |
0 |
0 |
0 |
0 |
1
|
0 |
0 |
1
|
ADGRB2
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
AMPD2
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
AMPD2, LOC126805822
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
AP5Z1, LOC129997864
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
AP5Z1, MIR4656
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
ARHGAP9, MARS1
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
CCT5
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
CEP63, KY
|
1
|
0 |
0 |
0 |
0 |
0 |
0 |
0 |
1
|
CYP7B1, LOC130000507
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
DNAJC16
|
0 |
0 |
0 |
0 |
0 |
1
|
0 |
0 |
1
|
FLRT1, MACROD1
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
GAD1
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
JAK3
|
0 |
0 |
0 |
0 |
0 |
1
|
0 |
0 |
1
|
KIF26A
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
0 |
1
|
LOC126860782, SETX
|
0 |
0 |
0 |
1
|
0 |
0 |
0 |
0 |
1
|
LOC129935332, PGAP1
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
LOC130056519, TECPR2
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
LOC130063377, PNPLA6
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
MIR6766, POLG
|
0 |
0 |
0 |
1
|
0 |
0 |
0 |
0 |
1
|
MYT1
|
0 |
0 |
0 |
0 |
0 |
1
|
0 |
0 |
1
|
NRG1
|
0 |
0 |
0 |
0 |
0 |
1
|
0 |
0 |
1
|
PLEKHG5
|
0 |
1
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
PTPN23
|
0 |
1
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
RETREG1
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
SH3TC2
|
0 |
1
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
SLC1A5
|
0 |
0 |
0 |
0 |
0 |
1
|
0 |
0 |
1
|
TUBB
|
0 |
0 |
0 |
0 |
0 |
1
|
0 |
0 |
1
|
WDR48
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
ZFR
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Submitter and significance breakdown #
Submitter |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
affects |
association |
not provided |
total |
Genome Diagnostics Laboratory, The Hospital for Sick Children
|
95
|
79
|
1071
|
337
|
226
|
0 |
0 |
0 |
1808
|
Invitae
|
0 |
0 |
67
|
44
|
23
|
0 |
0 |
0 |
134
|
Unit for Genetic & Epidemiological Research on Neurological Disorders, Instituto de Investigação e Inovação em Saúde
|
18
|
5
|
47
|
0 |
0 |
0 |
0 |
0 |
70
|
Women's Health and Genetics/Laboratory Corporation of America, LabCorp
|
19
|
17
|
0 |
0 |
0 |
0 |
0 |
0 |
36
|
Laboratory for Molecular Medicine, Mass General Brigham Personalized Medicine
|
8
|
2
|
0 |
0 |
0 |
0 |
0 |
0 |
10
|
Yunnan Provincial Key Laboratory of Clinical Virology, Institution of Basic and Clinical Medicine of Yunnan Province, The First People's Hospital of Yunnan Province
|
1
|
0 |
0 |
0 |
0 |
7
|
0 |
0 |
8
|
Paris Brain Institute, Inserm - ICM
|
3
|
0 |
0 |
0 |
0 |
0 |
0 |
0 |
3
|
Inherited Neuropathy Consortium
|
0 |
2
|
0 |
0 |
0 |
0 |
0 |
0 |
2
|
Center for Genomic Medicine, King Faisal Specialist Hospital and Research Center
|
0 |
1
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
Institute for Human Genetics and Genomic Medicine, Uniklinik RWTH Aachen
|
0 |
1
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
Neuromuscular disorders lab, University of Helsinki
|
1
|
0 |
0 |
0 |
0 |
0 |
0 |
0 |
1
|
Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
0 |
1
|
The Morris Kahn Laboratory of Human Genetics, Ben-Gurion University of the Negev
|
1
|
0 |
0 |
0 |
0 |
0 |
0 |
0 |
1
|
Kariminejad - Najmabadi Pathology & Genetics Center
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
New Leaf Center
|
0 |
1
|
0 |
0 |
0 |
0 |
0 |
0 |
1
|
Institute of Medical Genetics and Applied Genomics, University Hospital Tübingen
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Broad Center for Mendelian Genomics, Broad Institute of MIT and Harvard
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Molecular Genetics, Royal Melbourne Hospital
|
0 |
0 |
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Genetic Medicine Clinic, University Of Washington Medical Center
|
0 |
0 |
0 |
0 |
0 |
0 |
0 |
1
|
1
|
The information on this website is not intended for direct
diagnostic use or medical decision-making without review by a
genetics professional. Individuals should not change their
health behavior solely on the basis of information contained on
this website. Neither the University of Utah nor the National
Institutes of Health independently verfies the submitted
information. If you have questions about the information
contained on this website, please see a health care
professional.