If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
total |
22
|
14
|
3
|
0 |
3
|
42
|
Gene and significance breakdown #
Total genes and gene combinations: 34
Condition and significance breakdown #
Condition |
pathogenic |
likely pathogenic |
uncertain significance |
benign |
total |
Cerebellar-facial-dental syndrome
|
4
|
0 |
0 |
0 |
4
|
Amelogenesis imperfecta
|
0 |
0 |
0 |
3
|
3
|
Brachyolmia-amelogenesis imperfecta syndrome
|
3
|
0 |
0 |
0 |
3
|
Charlevoix-Saguenay spastic ataxia
|
0 |
2
|
0 |
0 |
2
|
Ectodermal dysplasia 10B, hypohidrotic/hair/tooth type, autosomal recessive
|
2
|
0 |
0 |
0 |
2
|
Intellectual disability, autosomal recessive 5
|
2
|
0 |
0 |
0 |
2
|
Junctional epidermolysis bullosa, non-Herlitz type
|
0 |
2
|
0 |
0 |
2
|
ACCES syndrome
|
1
|
0 |
0 |
0 |
1
|
Amelogenesis imperfecta hypomaturation type 2A3
|
1
|
0 |
0 |
0 |
1
|
Amelogenesis imperfecta hypomaturation type 2A5
|
1
|
0 |
0 |
0 |
1
|
Amelogenesis imperfecta type 1G
|
1
|
0 |
0 |
0 |
1
|
Autosomal recessive nonsyndromic hearing loss 93
|
0 |
1
|
0 |
0 |
1
|
CEBALID syndrome
|
0 |
1
|
0 |
0 |
1
|
Charcot-Marie-Tooth disease X-linked dominant 1
|
0 |
1
|
0 |
0 |
1
|
Charcot-Marie-Tooth disease type 4F
|
1
|
0 |
0 |
0 |
1
|
Charcot-Marie-Tooth disease, axonal, type 2EE
|
0 |
0 |
1
|
0 |
1
|
Christianson syndrome
|
0 |
1
|
0 |
0 |
1
|
Dyggve-Melchior-Clausen syndrome
|
1
|
0 |
0 |
0 |
1
|
Epidermolysis bullosa, junctional 3A, intermediate
|
0 |
1
|
0 |
0 |
1
|
Griscelli syndrome type 3
|
1
|
0 |
0 |
0 |
1
|
Hypomyelination and Congenital Cataract
|
0 |
1
|
0 |
0 |
1
|
Jalili syndrome
|
1
|
0 |
0 |
0 |
1
|
Kindler syndrome
|
0 |
1
|
0 |
0 |
1
|
Leukoencephalopathy, acute reversible, with increased urinary alpha-ketoglutarate
|
0 |
1
|
0 |
0 |
1
|
Li-Ghorbani-Weisz-Hubshman syndrome
|
0 |
1
|
0 |
0 |
1
|
Methylmalonic acidemia with homocystinuria, type cblX
|
0 |
1
|
0 |
0 |
1
|
Progressive pseudorheumatoid dysplasia
|
1
|
0 |
0 |
0 |
1
|
Recurrent metabolic encephalomyopathic crises-rhabdomyolysis-cardiac arrhythmia-intellectual disability syndrome
|
1
|
0 |
0 |
0 |
1
|
Rubinstein-Taybi syndrome due to CREBBP mutations
|
0 |
0 |
1
|
0 |
1
|
Stuttering, familial persistent, 4
|
0 |
0 |
1
|
0 |
1
|
Tooth agenesis
|
0 |
1
|
0 |
0 |
1
|
Tooth agenesis, selective, 4
|
1
|
0 |
0 |
0 |
1
|
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