If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
likely pathogenic, low penetrance |
total |
54
|
30
|
36
|
1
|
0 |
1
|
122
|
Gene and significance breakdown #
Total genes and gene combinations: 41
Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
likely pathogenic, low penetrance |
total |
FANCA
|
12
|
2
|
9
|
0 |
0 |
23
|
FANCG
|
5
|
2
|
2
|
0 |
0 |
9
|
MPL
|
4
|
4
|
1
|
0 |
0 |
9
|
AR
|
6
|
2
|
0 |
0 |
0 |
8
|
FANCD2, LOC107303338
|
0 |
1
|
6
|
0 |
0 |
7
|
TCF3
|
0 |
3
|
3
|
0 |
0 |
6
|
FANCA, ZNF276
|
1
|
0 |
4
|
0 |
0 |
5
|
SRD5A2
|
4
|
1
|
0 |
0 |
0 |
5
|
ITPKB
|
1
|
2
|
1
|
0 |
0 |
4
|
NR5A1
|
1
|
2
|
0 |
0 |
0 |
3
|
PDGFRA
|
1
|
2
|
0 |
0 |
0 |
3
|
PTEN
|
1
|
2
|
0 |
0 |
0 |
3
|
RTEL1, RTEL1-TNFRSF6B
|
0 |
0 |
3
|
0 |
0 |
3
|
DCLRE1B
|
2
|
0 |
0 |
0 |
0 |
2
|
FANCD2, FANCD2OS
|
0 |
0 |
2
|
0 |
0 |
2
|
FANCI
|
2
|
0 |
0 |
0 |
0 |
2
|
ITPKB, LOC129932672
|
0 |
1
|
0 |
1
|
0 |
2
|
NOTCH1
|
2
|
0 |
0 |
0 |
0 |
2
|
TERT
|
2
|
0 |
0 |
0 |
0 |
2
|
AR, LOC109504725
|
1
|
0 |
0 |
0 |
0 |
1
|
BLM
|
1
|
0 |
0 |
0 |
0 |
1
|
BRCA2
|
1
|
0 |
0 |
0 |
0 |
1
|
DHX37
|
0 |
1
|
0 |
0 |
0 |
1
|
DMRT2
|
0 |
0 |
1
|
0 |
0 |
1
|
FANCA, LOC130059837
|
1
|
0 |
0 |
0 |
0 |
1
|
FANCA, SPIRE2
|
0 |
0 |
1
|
0 |
0 |
1
|
FANCB
|
0 |
0 |
1
|
0 |
0 |
1
|
FANCC
|
1
|
0 |
0 |
0 |
0 |
1
|
FANCE
|
0 |
0 |
1
|
0 |
0 |
1
|
FANCF
|
1
|
0 |
0 |
0 |
0 |
1
|
HSD17B3, SLC35D2-HSD17B3
|
0 |
0 |
1
|
0 |
0 |
1
|
LMBRD1
|
1
|
0 |
0 |
0 |
0 |
1
|
LOC126807054, PDGFRA
|
0 |
1
|
0 |
0 |
0 |
1
|
LOC130003020, NOTCH1
|
1
|
0 |
0 |
0 |
0 |
1
|
M1AP
|
0 |
0 |
0 |
0 |
1
|
1
|
NF1
|
1
|
0 |
0 |
0 |
0 |
1
|
RP1
|
0 |
1
|
0 |
0 |
0 |
1
|
RPS26
|
0 |
1
|
0 |
0 |
0 |
1
|
SLCO2A1
|
0 |
1
|
0 |
0 |
0 |
1
|
TINF2
|
0 |
1
|
0 |
0 |
0 |
1
|
TYR
|
1
|
0 |
0 |
0 |
0 |
1
|
Condition and significance breakdown #
Condition |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
likely pathogenic, low penetrance |
total |
Fanconi anemia
|
24
|
5
|
26
|
0 |
0 |
55
|
Myeloproliferative neoplasm, unclassifiable
|
7
|
11
|
4
|
1
|
0 |
23
|
Androgen resistance syndrome
|
7
|
2
|
0 |
0 |
0 |
9
|
Congenital amegakaryocytic thrombocytopenia
|
4
|
4
|
1
|
0 |
0 |
9
|
3-Oxo-5 alpha-steroid delta 4-dehydrogenase deficiency
|
4
|
1
|
0 |
0 |
0 |
5
|
46,XY sex reversal 3
|
1
|
2
|
0 |
0 |
0 |
3
|
Fanconi anemia complementation group C
|
2
|
0 |
0 |
0 |
0 |
2
|
Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 3
|
0 |
0 |
2
|
0 |
0 |
2
|
46,XY sex reversal 11
|
0 |
1
|
0 |
0 |
0 |
1
|
Bloom syndrome
|
1
|
0 |
0 |
0 |
0 |
1
|
Diamond-Blackfan anemia 10
|
0 |
1
|
0 |
0 |
0 |
1
|
Dyskeratosis congenita, autosomal dominant 2
|
1
|
0 |
0 |
0 |
0 |
1
|
Dyskeratosis congenita, autosomal dominant 3
|
0 |
1
|
0 |
0 |
0 |
1
|
Dyskeratosis congenita, autosomal recessive 5
|
0 |
0 |
1
|
0 |
0 |
1
|
Gonadal agenesis
|
0 |
0 |
1
|
0 |
0 |
1
|
Hypertrophic osteoarthropathy, primary, autosomal recessive, 2
|
0 |
1
|
0 |
0 |
0 |
1
|
Methylmalonic aciduria and homocystinuria type cblF
|
1
|
0 |
0 |
0 |
0 |
1
|
Oculocutaneous albinism type 1B
|
1
|
0 |
0 |
0 |
0 |
1
|
Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1
|
1
|
0 |
0 |
0 |
0 |
1
|
Retinitis pigmentosa 1
|
0 |
1
|
0 |
0 |
0 |
1
|
Spermatogenic failure 48
|
0 |
0 |
0 |
0 |
1
|
1
|
Testosterone 17-beta-dehydrogenase deficiency
|
0 |
0 |
1
|
0 |
0 |
1
|
The information on this website is not intended for direct
diagnostic use or medical decision-making without review by a
genetics professional. Individuals should not change their
health behavior solely on the basis of information contained on
this website. Neither the University of Utah nor the National
Institutes of Health independently verfies the submitted
information. If you have questions about the information
contained on this website, please see a health care
professional.