If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
55
|
32
|
320
|
108
|
42
|
14
|
556
|
Gene and significance breakdown #
Total genes and gene combinations: 16
Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
SPG11
|
23
|
9
|
160
|
32
|
10
|
13
|
239
|
ALS2
|
15
|
14
|
82
|
12
|
21
|
0 |
141
|
SIGMAR1
|
6
|
7
|
54
|
56
|
7
|
0 |
126
|
LOC130001681, SIGMAR1
|
5
|
0 |
15
|
8
|
3
|
0 |
31
|
ALS2, LOC129935419
|
0 |
0 |
2
|
0 |
1
|
0 |
3
|
FUS
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
LOC130056971, SPG11
|
0 |
0 |
2
|
0 |
0 |
0 |
2
|
LOC130056973, SPG11
|
0 |
0 |
2
|
0 |
0 |
0 |
2
|
PLEKHG5
|
1
|
1
|
0 |
0 |
0 |
0 |
2
|
SYNE1
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
ARHGEF39, ARID3C, ATOSB, CA9, CCDC107, CCIN, CCL19, CCL21, CCL27, CD72, CIMIP2B, CLTA, CNTFR, CREB3, DCTN3, DNAI1, DNAJB5, ENHO, FAM221B, FANCG, GALT, GBA2, GLIPR2, GNE, HINT2, HRCT1, IL11RA, MSMP, NPR2, OR13J1, OR2S2, PHF24, PIGO, RECK, RGP1, RMRP, RPP25L, RUSC2, SIGMAR1, SIT1, SPAG8, SPATA31F1, SPATA31G1, STOML2, TESK1, TLN1, TMEM8B, TPM2, UNC13B, VCP
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
ARID3C, CCL19, CCL21, CCL27, CNTFR, DCTN3, DNAI1, DNAJB5, ENHO, GALT, IL11RA, PHF24, RPP25L, SIGMAR1, SPATA31F1, SPATA31G1, VCP
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
ERLIN1
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
TRPM7
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
TRPV4
|
0 |
0 |
0 |
0 |
0 |
1
|
1
|
VRK1
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
Submitter and significance breakdown #
Submitter |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
Genome-Nilou Lab
|
4
|
2
|
151
|
30
|
19
|
0 |
206
|
Labcorp Genetics (formerly Invitae), Labcorp
|
10
|
3
|
69
|
63
|
10
|
0 |
155
|
Illumina Laboratory Services, Illumina
|
0 |
0 |
79
|
9
|
17
|
0 |
105
|
Fulgent Genetics, Fulgent Genetics
|
10
|
4
|
15
|
7
|
2
|
0 |
38
|
Suna and Inan Kirac Foundation Neurodegeneration Research Laboratory, Koc University
|
11
|
7
|
1
|
0 |
0 |
0 |
19
|
Baylor Genetics
|
6
|
1
|
10
|
0 |
0 |
0 |
17
|
GenomeConnect - Invitae Patient Insights Network
|
0 |
0 |
0 |
0 |
0 |
14
|
14
|
OMIM
|
11
|
0 |
1
|
0 |
0 |
0 |
12
|
Victorian Clinical Genetics Services, Murdoch Childrens Research Institute
|
1
|
1
|
1
|
0 |
0 |
0 |
3
|
Center for Genomic Medicine, King Faisal Specialist Hospital and Research Center
|
2
|
1
|
0 |
0 |
0 |
0 |
3
|
Hadassah Hebrew University Medical Center
|
0 |
3
|
0 |
0 |
0 |
0 |
3
|
GeneReviews
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
NeuroMeGen, Hospital Clinico Santiago de Compostela
|
0 |
2
|
0 |
0 |
0 |
0 |
2
|
Centre for Mendelian Genomics, University Medical Centre Ljubljana
|
0 |
2
|
0 |
0 |
0 |
0 |
2
|
Institute of Human Genetics, University of Leipzig Medical Center
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
Juno Genomics, Hangzhou Juno Genomics, Inc
|
0 |
0 |
2
|
0 |
0 |
0 |
2
|
Broad Center for Mendelian Genomics, Broad Institute of MIT and Harvard
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
Medical Genetics, Christian Medical College
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
3billion
|
0 |
2
|
0 |
0 |
0 |
0 |
2
|
Institute of Human Genetics, Clinical Exome/Genome Diagnostics Group, University Hospital Bonn
|
0 |
2
|
0 |
0 |
0 |
0 |
2
|
MGZ Medical Genetics Center
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
Centogene AG - the Rare Disease Company
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
Mendelics
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Soonchunhyang University Bucheon Hospital, Soonchunhyang University Medical Center
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
Genomic Medicine Lab, University of California San Francisco
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Pathology and Clinical Laboratory Medicine, King Fahad Medical City
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
Coyote Medical Laboratory (Beijing), Coyote
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
Section for Clinical Neurogenetics, University of Tübingen
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
Molecular Genetics Lab, CHRU Brest
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Suma Genomics
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
Neuberg Centre For Genomic Medicine, NCGM
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
Igenomix - Part of Vitrolife Group, Igenomix
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
The information on this website is not intended for direct
diagnostic use or medical decision-making without review by a
genetics professional. Individuals should not change their
health behavior solely on the basis of information contained on
this website. Neither the University of Utah nor the National
Institutes of Health independently verfies the submitted
information. If you have questions about the information
contained on this website, please see a health care
professional.